Abstract. ESTOPINAN REBOLLAR, Ramón; ESTOPINAN CANOVAS, Ramón and PILA PELAEZ, Rafael. Enfermedad de Hirschsprung en un adulto. Rev Col. Resumen. LOMBANA, Luis Jorge y DOMINGUEZ, Luis Carlos. Surgery in adult Hirschsprung’s disease. Rev Col Gastroenterol [online]. , vol, n La enfermedad de Hirschsprung es una enfermedad del intestino grueso (colon). Normalmente, las heces fecales son empujadas a través del colon por.

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Cirugía en la enfermedad de Hirschsprung del adulto

Enfermedad de Hirschsprung en el adulto. When he arrived at the hospital, he told doctors that he had not had a bowel movement for 83 days. The girl refers onset of fecal incontinence at the age of Hirschsprung’s Disease HDalso known as congenital aganglionic megacolon, is an anomaly characterized by an absence of ganglion cells in the myenteric and submucosal plexuses in a variable bowel segment. Print Send to a friend Export reference Mendeley Statistics. Standing and prone abdominal radiography showed x-ray opacity compatible with adulots matter.

In adults, the treatment of choice is the Duhamel operation, which results in reduced fecal impaction after the procedure.

Conventional anorectal manometry trace showing the absence of the inhibitory rectoanal reflex with the hirschspprung tolerable rectal capacity. Aganglionic segment remains permanently contracted, while proximal segment retains peristalsis, resulting in hypertrophy, megacolon and sometimes perforation of normally innervated segment 2. This surgery is considered curative.

With this technique an extensive dissection of the anterior wall of the enfermedas is avoided, thus avoiding the risk of injuring adjacent structures.


Rectum had a normal size. Approximately cases have been reported in literature. He is awaiting surgical intervention. Hirschsprung Disease HD or Congenital Megacolon is an anomaly that is characterized mainly for the absence of ganglion cells in the myenteric plexus and submucosal in a variable segment of the intestine.

This clinical course is atypical; in the literature review, only three similar cases were related in association with Hirschsprung disease. SJR uses a similar algorithm as the Google page rank; it provides a quantitative and qualitative measure of the journal’s impact. Hirschsprung’s disease is characterized by absence of ganglion cells in submucosal and myenteric plexus of distal bowel.

The principal aim of the journal is to publish original work in the broad field of Gastroenterology, as well as to provide information on the specialty and related areas that is up-to-date and relevant.

It is important to consider the presence of this rare pathologic process in young adult patients with treatment-refractory chronic constipation, in whom other more common diseases have been ruled out through easily accessed studies, such as imaging or anorectal physiology studies. The diagnosis of HD in adults is much harder than in children, due to their rarity as they are often short or ultrashort aganglionic segments, which produce mild symptoms in early stages of the disease.

The journal accepts original articles, scientific letters, review articles, clinical guidelines, consensuses, editorials, letters to the Editors, brief communications, and clinical images in Gastroenterology in Spanish and English for their publication.

Rev Esp Enferm Dig, 3pp. It usually presents as severe constipation with colonic dilatation proximal to aduptos aganglionic segment. HD presents itself by symptoms of constipation, such as a greater than h delay in elimination of meconium, abdominal distention and vomiting.


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The choice of either technique will depend on hirschspfung condition of patient and abdominal conditions existence of pollution, peritonitis, etc.

Rev Gastroenterol Mex, 65pp. Typically, patients go to the doctor with a long-standing history of constipation requiring frequent laxative use.

It is the most hirscbsprung cause of the lower neonatal intestinal obstruction. These patients tend to have milder forms of the disease, in which hypertrophy of innervated proximal colon compensates the functional obstruction by lack of innervation of the distal area 2.

Hospital Universitario Virgen Macarena.

Vólvulo en adultos

HD occurs in approximately 1 in live births. The patient suffered from sensory aphasia episode, being diagnosed with ischemic stroke, with good recuperation without sequelae.

Adult segmental Hirschsprung disease. A resection of distal rectal mucosa of the aganglionic segment is performed, maintaining muscular wall of this segment. No abnormalities resulted from the rectal examination.

Diagnóstico tardio da doenc¸a de Hirschsprung

Clinical response in Mexican patients enfdrmedad irritable bowel Postoperative evolution was torpid, with difficulty feedback by adynamic ileus and infection of surgical wound. A year-old male was admitted in the Emergency Department by generalized abdominal pain accompanied by anorexia of several days duration.

Several procedures have been designed to treat HD, of which the most important are the following 7: