A frequência da Anomalia de Ebstein encontrada foi semelhante a de outros Centros. A técnica de Cone foi viável na maior parte dos pacientes. A mortalidade. Ebstein’s anomaly is a malformation of the tricuspid valve. In this defect, there is a downward displacement of the tricuspid valve (located between the upper and. Antecedentes: en la actualidad, con la ecocardiografía fetal, es pos ble confirmar el diagnóstico in utero de la anomalía de Ebstein y determinar, con certeza.
|Published (Last):||21 December 2005|
|PDF File Size:||4.9 Mb|
|ePub File Size:||14.78 Mb|
|Price:||Free* [*Free Regsitration Required]|
Prenatal diagnosis of Down’s syndrome in the presence of isolated Ebstein’s anomaly. All patients underwent surgical intervention. J Ebstekn Cardiovasc Surg, 96pp. Differential diagnosis The major differential diagnosis, particularly during fetal life, is dysplasia of the leaflets of the tricuspid valve.
Introduction and Objective Ebstein’s anomaly is a rare complex congenital heart defect of ebsteni tricuspid valve. The cone reconstruction of the tricuspid valve in Ebstein’s anomaly.
Additional information Further information on this disease Classification s 3 Gene s 1 Clinical signs and symptoms Publications in PubMed Other website s 3. Thank you for your patience. Cardiol Young, 14pp.
The third patient showed the greatest improvement Figure 3. This study revealed that 0.
Anomalía de Ebstein en niños
Prognosis Asymptomatic patients, and patients with mild forms of the disease, have a normal life expectancy. The clinical profile of Ebstein’s malformation as seen from the fetus to the adult in 52 patients. Cardiothoracic index, echocardiographic findings, surgical indications, surgery performed and early post-operative evaluation.
The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment. Xe treatment relies on inotropic agents in case of cardiac failure and antiarrhythmic drugs in case of tachyarrhythmia.
Chest X-rays showing an impressive reduction in cardiothoracic index after cone reconstruction. The MyHealth mobile app puts all your health information at your fingertips and makes managing your health care simple and quick.
Several techniques have been described to avoid this complication. Female gender was predominant, with a female: Cardiothoracic index, echocardiographic findings, surgical indications, surgery performed and early post-operative evaluation.
Clinical and echocardiographic features of Ebstein’s malformation in Sudanese patients. All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Attribution License.
New York Heart Association. Congenit Heart Dis, 9pp. J Am Coll Cardiol, 3pp. Clinical presentation is heterogeneous and depends on the severity of the lesion extent of tethering of the antero-superior leaflet across the normal valvar orificeand the degree of dysfunction of the right ventricle. Data on X-ray, echocardiography, indications for surgery, type of surgical techniques and complications are presented in Table Specialised Social Services Eurordis directory.
Mostrar mais Mostrar menos. Two-dimensional echocardiographic spectrum of Ebstein’s anomaly: Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted. See a Stanford specialist to learn about your treatment options. Conclusion The frequency of Ebstein’s anomaly was similar to that in other centers. An international co-operative study of cases. Evolution of cardiothoracic index in the five patients undergoing cone reconstruction.
J Am Coll Cardiol ; The corresponding author is in possession of this document. The severest forms of Ebstein’s malformation can produce an imperforate tricuspid valve, which must be distinguished from tricuspid atresia see this term. Definitive treatment is surgical and consists of reconstructive surgery prior to the onset of cardiac failure.
Orphanet: Anomalia de Ebstein
Infective endocarditis in an HIV-infected intravenous drug Mosby-Year Book, ; Am J Med Genet A,pp. Diagnostic methods Diagnosis is based on cross-sectional or 3D echocardiography, which reveals the rotational displacement of the leaflets, the extent of abnormal tethering of the antero-superior leaflet, the extent of thinning of the atrialized inlet component of the right ventricle, and the degree of regurgitation or stenosis of the abnormal valve.
The authors have no conflicts of interest to declare. In this defect, there is a downward displacement of the tricuspid valve located between the upper and lower chambers on the right side of the heart into the right bottom chamber of the heart or right ventricle.
Our patients had access to medical care at a critical stage of the disease. MyHealth for Mobile The MyHealth mobile app puts all your health information at your fingertips and makes managing your health care simple and quick.
On the other hand, Arizmendi et al. Br Heart J ;